ACTA1 Antibody
Product Sizes
100ul
£392.00
OASG07751-100UL
About this Product
- SKU:
- OASG07751
- Additional Names:
- ACTA; ASMA; CFTD; MPFD; NEM1; NEM2; NEM3; SHPM; CFTD1; CFTDM
- Clonality:
- Monoclonal
- Concentration:
- 1 mg/ml
- Extra Details:
- The product encoded by this gene belongs to the actin family of proteins; which are highly conserved proteins that play a role in cell motility; structure and integrity. Alpha; beta and gamma actin isoforms have been identified; with alpha actins being a major constituent of the contractile apparatus; while beta and gamma actins are involved in the regulation of cell motility. This actin is an alpha actin that is found in skeletal muscle. Mutations in this gene cause nemaline myopathy type 3; congenital myopathy with excess of thin myofilaments; congenital myopathy with cores; and congenital myopathy with fiber-type disproportion; diseases that lead to muscle fiber defects.
- Gene Details:
- actin; alpha 1; skeletal muscle
- Host:
- Mouse
- Immunogen:
- Synthetic Peptide of Muscle actin
- Isotype:
- IgG1
- Protein Details:
- Actin; alpha skeletal muscle
- Purification:
- The antibody was affinity-purified from mouse ascites by affinity-chromatography using specific immunogen.
- Shipping Conditions:
- Blue Ice
- Storage Conditions:
- Store at -20C. Avoid repeated freeze/thaw cycles.
- Supplier:
- Aviva Systems Biology
- Type:
- Antibodies: Monoclonal Antibody
- Manufacturer's Data Sheet:html_datasheet.php
