ALDH6A1 Antibody
Product Sizes
100ul
£630.00
OAGA04712-100UL
About this Product
- SKU:
- OAGA04712
- Additional Names:
- MMSDH; MMSADHA
- Clonality:
- Polyclonal
- Concentration:
- 0.63 mg/ml
- Extra Details:
- This gene encodes a member of the aldehyde dehydrogenase protein family. The encoded protein is a mitochondrial methylmalonate semialdehyde dehydrogenase that plays a role in the valine and pyrimidine catabolic pathways. This protein catalyzes the irreversible oxidative decarboxylation of malonate and methylmalonate semialdehydes to acetyl- and propionyl-CoA. Methylmalonate semialdehyde dehydrogenase deficiency is characterized by elevated beta-alanine; 3-hydroxypropionic acid; and both isomers of 3-amino and 3-hydroxyisobutyric acids in urine organic acids. Alternate splicing results in multiple transcript variants.
- Gene Details:
- aldehyde dehydrogenase 6 family member A1
- Host:
- Rabbit
- Immunogen:
- Recombinant protein encompassing a sequence within the center region of human ALDH6A1. The exact sequence is proprietary.
- Isotype:
- IgG
- Protein Details:
- methylmalonate-semialdehyde dehydrogenase [acylating]; mitochondrial
- Purification:
- Purified by antigen-affinity chromatography.
- Shipping Conditions:
- Blue Ice
- Storage Conditions:
- Keep as concentrated solution. Aliquot and store at -20C or below. Avoid multiple freeze-thaw cycles.
- Supplier:
- Aviva Systems Biology
- Type:
- Antibodies: Polyclonal Antibody
- Manufacturer's Data Sheet:html_datasheet.php
