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Antibodies

ATXN3 Antibody

Product Sizes
100 uL
£446.00
OAAJ06849-100UL
About this Product
SKU:
OAAJ06849
Additional Names:
AT3; JOS; MJD; ATX3; MJD1; SCA3
Clonality:
Polyclonal
Concentration:
1 mg/mL
Extra Details:
Deubiquitinating enzyme involved in protein homeostasis maintenance; transcription; cytoskeleton regulation; myogenesis and degradation of misfolded chaperone substrates. Binds long polyubiquitin chains and trims them; while it has weak or no activity against chains of 4 or less ubiquitins. Involved in degradation of misfolded chaperone substrates via its interaction with STUB1/CHIP: recruited to monoubiquitinated STUB1/CHIP; and restricts the length of ubiquitin chain attached to STUB1/CHIP substrates and preventing further chain extension. In response to misfolded substrate ubiquitination; mediates deubiquitination of monoubiquitinated STUB1/CHIP. Interacts with key regulators of transcription and represses transcription: acts as a histone-binding protein that regulates transcription.
Host:
Rabbit
Immunogen:
Recombinant proteinof human ATXN3
Molecular Weight:
43 kDa
Protein Details:
Ataxin-3
Purification:
Immunogen affinity chromatography
Shipping Conditions:
Blue Ice
Storage Conditions:
Store at +4C. For long term storage; aliquot and store at -20C. Avoid freeze/thaw cycles.
Supplier:
Aviva Systems Biology
Type:
Antibodies: Polyclonal Antibody