PEX19 Antibody - middle region
Product Sizes
25ul
£177.00
ARP81359-P050-25UL
100 ul
£412.00
ARP81359-P050-100UL
About this Product
- SKU:
- ARP81359-P050
- Additional Names:
- PXF; HK33; PMP1; PMPI; PXMP1; PBD12A; D1S2223E
- Clonality:
- Polyclonal
- Concentration:
- 0.5 mg/ml
- Extra Details:
- This gene is necessary for early peroxisomal biogenesis. It acts both as a cytosolic chaperone and as an import receptor for peroxisomal membrane proteins (PMPs). Peroxins (PEXs) are proteins that are essential for the assembly of functional peroxisomes. The peroxisome biogenesis disorders (PBDs) are a group of genetically heterogeneous autosomal recessive; lethal diseases characterized by multiple defects in peroxisome function. These disorders have at least 14 complementation groups; with more than one phenotype being observed for some complementation groups. Although the clinical features of PBD patients vary; cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene are a cause of Zellweger syndrome (ZWS); as well as peroxisome biogenesis disorder complementation group 14 (PBD-CG14); which is also known as PBD-CGJ. Alternative splicing results in multiple transcript variants.
- Gene Details:
- peroxisomal biogenesis factor 19
- Host:
- Rabbit
- Immunogen:
- The immunogen is a synthetic peptide directed towards the middle region of human PEX19
- Molecular Weight:
- 33 kDa
- Protein Details:
- peroxisomal biogenesis factor 19
- Purification:
- Affinity purified
- Shipping Conditions:
- Blue Ice
- Storage Conditions:
- For short term use; store at 2-8C up to 1 week. For long term storage; store at -20C in small aliquots to prevent freeze-thaw cycles.
- Supplier:
- Aviva Systems Biology
- Type:
- Antibodies: Polyclonal Antibody
- Manufacturer's Data Sheet:html_datasheet.php
