Peroxin 7 rabbit pAb
Product Sizes
50UL
£ POA
ES6572-50UL
100UL
£ POA
ES6572-100UL
About this Product
- SKU:
- ES6572
- Additional Names:
- PEX7; PTS2R; Peroxisomal targeting signal 2 receptor; PTS2 receptor; Peroxin-7
- Application:
- Western Blot, Immunohistochemistry, Immunofluorescence, ELISA
- Clonality:
- Polyclonal
- Concentration:
- 1 mg/ml
- Extra Details:
- This gene encodes the cytosolic receptor for the set of peroxisomal matrix enzymes targeted to the organelle by the peroxisome targeting signal 2 (PTS2). Defects in this gene cause peroxisome biogenesis disorders (PBDs); which are characterized by multiple defects in peroxisome function. There are at least 14 complementation groups for PBDs; with more than one phenotype being observed in cases falling into particular complementation groups. Although the clinical features of PBD patients vary; cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene have been associated with PBD complementation group 11 (PBD-CG11) disorders; rhizomelic chondrodysplasia punctata type 1 (RCDP1); and Refsum disease (RD). [provided by RefSeq; Oct 2008];
- Immunogen:
- The antiserum was produced against synthesized peptide derived from human PEX7. AA range:204-253
- Isotype:
- IgG
- Reactivities:
- Human, Mouse, Rat
- Shipping Conditions:
- Blue Ice
- Source:
- Rabbit
- Storage Conditions:
- -20[o]C
- Supplier:
- ELK Biotechnology
- Type:
- Antibodies: Polyclonal Antibody
