VMA21 Polyclonal Antibody
Product Sizes
20 ul
£118.00
E-AB-53204-20UL
60 ul
£183.00
E-AB-53204-60UL
120 ul
£272.00
E-AB-53204-120UL
200 ul
£420.00
E-AB-53204-200UL
About this Product
- SKU:
- E-AB-53204
- Additional Names:
- Vacuolar ATPase Assembly Factor,MEAX,Myopathy With Excessive Autophagy,Myopathy With Excessive Autophagy Protein,VMA21,VMA21 Vacuolar H+-ATPase,VMA21 Vacuolar H+-ATPase Homolog (S. Cerevisiae),Vacuolar ATPase Assembly Integral Membrane Protein VMA21,XMEA
- Application:
- Immunofluorescence, Immunohistochemistry
- Buffer:
- Phosphate buffered solution, pH 7.4, containing 0.05% stabilizer and 50% glycerol.
- Clonality:
- Polyclonal
- Concentration:
- 2.6 mg/ml
- Extra Details:
- This gene encodes a chaperone for assembly of lysosomal vacuolar ATPase. Required for the assembly of the V0 complex of the vacuolar ATPase (V-ATPase) in the endoplasmic reticulum. Associates with the V0 complex of the vacuolar ATPase (V-ATPase). MEAX is a childhood-onset disease characterized by progressive vacuolation and atrophy of skeletal muscle. It is inherited in recessive fashion, affecting boys and sparing carrier females. Onset is in childhood, and patients exhibit weakness of the proximal muscles of the lower extremities, progressing slowly to involve other skeletal muscle groups over time.
- Host:
- Rabbit
- Immunogen:
- Synthetic peptide of human VMA21
- Isotype:
- IgG
- Purification:
- Affinity Purified
- Reactivities:
- Human, Mouse
- Shipping Conditions:
- Blue Ice
- Storage Conditions:
- -20[o]C Avoid freeze/thaw cycles.
- Supplier:
- Elabscience
- Type:
- Antibody: Polyclonal Antibody
- Manufacturer's Data Sheet:p-vma21_polyclonal_antibody-e_ab_53204
