CLCN7 Polyclonal Antibody
Product Sizes
20 ul
£118.00
E-AB-52548-20UL
60 ul
£183.00
E-AB-52548-60UL
120 ul
£272.00
E-AB-52548-120UL
200 ul
£420.00
E-AB-52548-200UL
About this Product
- SKU:
- E-AB-52548
- Additional Names:
- CLC 7,CLCN7,Chloride channel protein 7,ClC-7,ClC7,FLJ26686,FLJ39644,FLJ46423,H(+)/Cl(-) exchange transporter 7,OPTA2,OPTB4
- Application:
- Immunohistochemistry
- Buffer:
- Phosphate buffered solution, pH 7.4, containing 0.05% stabilizer and 50% glycerol.
- Clonality:
- Polyclonal
- Concentration:
- 1.56 mg/ml
- Extra Details:
- The product of this gene belongs to the CLC chloride channel family of proteins. Chloride channels play important roles in the plasma membrane and in intracellular organelles. This gene encodes chloride channel 7. Defects in this gene are the cause of osteopetrosis autosomal recessive type 4 (OPTB4), also called infantile malignant osteopetrosis type 2 as well as the cause of autosomal dominant osteopetrosis type 2 (OPTA2), also called autosomal dominant Albers-Schonberg disease or marble disease autosoml dominant. Osteopetrosis is a rare genetic disease characterized by abnormally dense bone, due to defective resorption of immature bone. OPTA2 is the most common form of osteopetrosis, occurring in adolescence or adulthood.
- Host:
- Rabbit
- Immunogen:
- Fusion protein of human CLCN7
- Isotype:
- IgG
- Purification:
- Affinity Purified
- Reactivities:
- Human, Mouse, Rat
- Shipping Conditions:
- Blue Ice
- Storage Conditions:
- -20[o]C Avoid freeze/thaw cycles.
- Supplier:
- Elabscience
- Type:
- Antibody: Polyclonal Antibody
- Manufacturer's Data Sheet:p-clcn7_polyclonal_antibody-e_ab_52548
