ASS1 Polyclonal Antibody
Product Sizes
20 ul
£118.00
E-AB-18521-20UL
60 ul
£183.00
E-AB-18521-60UL
120 ul
£272.00
E-AB-18521-120UL
200 ul
£420.00
E-AB-18521-200UL
About this Product
- SKU:
- E-AB-18521
- Additional Names:
- ASS,ASSA,ASSY,Argininosuccinate synthase,Argininosuccinate synthase 1,Argininosuccinate synthetase 1,Ass-1,CTLN1,Citrulline aspartate ligase,Citrulline--aspartate ligase,ass1
- Application:
- Immunohistochemistry, Western Blot
- Buffer:
- Phosphate buffered solution, pH 7.4, containing 0.05% stabilizer and 50% glycerol.
- Clonality:
- Polyclonal
- Concentration:
- 0.5 mg/ml
- Extra Details:
- ASS1 is a rate-limiting enzyme in the urea cycle. Citrullinemia type I is an autosomal recessive disorder that is caused by a deficiency of the urea cycle enzyme argininosuccinate synthetase (ASS1). Deficiency of ASS1 shows various clinical manifestations encompassing severely affected patients with fatal neonatal hyperammonemia as well as asymptomatic individuals with only a biochemical phenotype.
- Host:
- Rabbit
- Immunogen:
- Fusion protein of human ASS1
- Isotype:
- IgG
- Purification:
- Affinity Purified
- Reactivities:
- Human, Mouse, Rat
- Shipping Conditions:
- Blue Ice
- Storage Conditions:
- -20[o]C Avoid freeze/thaw cycles.
- Supplier:
- Elabscience
- Type:
- Antibody: Polyclonal Antibody
- Manufacturer's Data Sheet:p-ass1_polyclonal_antibody-e_ab_18521
