FH Polyclonal Antibody
Product Sizes
20 ul
£118.00
E-AB-11249-20UL
60 ul
£183.00
E-AB-11249-60UL
120 ul
£272.00
E-AB-11249-120UL
200 ul
£420.00
E-AB-11249-200UL
About this Product
- SKU:
- E-AB-11249
- Additional Names:
- FH,FUMH,Fumarase,Fumarate hydratase,Fumarate hydratase mitochondrial,HLRCC,LRCC,MCL,MCUL 1,MCUL1,MS709,Multiple hereditary cutaneous leiomyomata,mitochondrial
- Application:
- Immunohistochemistry, Western Blot
- Buffer:
- Phosphate buffered solution, pH 7.4, containing 0.05% stabilizer and 50% glycerol.
- Clonality:
- Polyclonal
- Concentration:
- 0.5 mg/ml
- Extra Details:
- The protein encoded by this gene is an enzymatic component of the tricarboxylic acid (TCA) cycle, or Krebs cycle, and catalyzes the formation of L-malate from fumarate. It exists in both a cytosolic form and an N-terminal extended form, differing only in the translation start site used. The N-terminal extended form is targeted to the mitochondrion, where the removal of the extension generates the same form as in the cytoplasm. It is similar to some thermostable class II fumarases and functions as a homotetramer. Mutations in this gene can cause fumarase deficiency and lead to progressive encephalopathy.
- Host:
- Rabbit
- Immunogen:
- Recombinant protein of human FH
- Isotype:
- IgG
- Purification:
- Affinity Purified
- Reactivities:
- Human, Mouse, Rat
- Shipping Conditions:
- Blue Ice
- Storage Conditions:
- -20[o]C Avoid freeze/thaw cycles.
- Supplier:
- Elabscience
- Type:
- Antibody: Polyclonal Antibody
- Manufacturer's Data Sheet:p-fh_polyclonal_antibody-e_ab_11249
