Recombinant SPR Monoclonal Antibody
Product Sizes
50 ul
£281.00
AN302028L-50UL
100 ul
£402.00
AN302028L-100UL
About this Product
- SKU:
- AN302028L
- Additional Names:
- SDR38C;member;OTTHUMP;SPR;SDR38C1;8 dihydrobiopterin:NADP+ oxidoreductase);member 1;OTTHUMP00000160199;Sepiapterin reductase;Sepiapterin reductase (7;Short chain dehydrogenase/reductase family 38C;SPRE
- Application:
- Immunohistochemistry, Western Blot
- Buffer:
- PBS, 50% glycerol, 0.05% Proclin 300, 0.05% protein protectant.
- translate.label.attr.clone:
- A748
- Clonality:
- Recombinant Monoclonal
- Concentration:
- 1 mg/ml
- Extra Details:
- SPR can catalyze the final one or two reductions in tetra-hydrobiopterin biosynthesis to form 5,6,7,8-tetrahydrobiopterin.Defects in SPR are the cause of dystonia DOPA-responsive due to sepiapterin reductase deficiency (DRDSPRD). In the majority of cases, patients manifest progressive psychomotor retardation, dystonia and spasticity. Cognitive anomalies are also often present. The disease is due to severe dopamine and serotonin deficiencies in the central nervous system caused by a defect in BH4 synthesis.
- Host:
- Rabbit
- Immunogen:
- Peptide. This information is proprietary to PTMab.
- Isotype:
- IgG, kappa
- Purification:
- Protein A Purified
- Reactivities:
- Human
- Shipping Conditions:
- Blue Ice
- Storage Conditions:
- -20[o]C Avoid freeze/thaw cycles.
- Supplier:
- Elabscience
- Type:
- Antibody: Recombinant Antibodies
- Manufacturer's Data Sheet:p-recombinant_spr_monoclonal_antibody-an302028l
