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Antibodies

CEP290 Antibody

Product Sizes
100 ul
£332.00
CSB-PA758165-100UL
About this Product
SKU:
CSB-PA758165
Additional Names:
3H11AG antibody; Bardet-Biedl syndrome 14 protein antibody; BBS14 antibody; Cancer/testis antigen 87 antibody; CE290_HUMAN antibody; Centrosomal protein 290 antibody; Centrosomal protein 290kDa antibody; Centrosomal protein of 290 kDa antibody; Cep290 antibody; CT87 antibody; CTCL tumor antigen se2 2 antibody; FLJ13615 antibody; FLJ21979 antibody; JBTS5 antibody; JBTS6 antibody; KIAA0373 antibody; LCA10 antibody; Meckel syndrome; type 4 antibody; MKS4 antibody; Monoclonal antibody 3H11 antigen antibody; Nephrocystin 6 antibody; Nephrocystin-6 antibody; NPHP6 antibody; POC3 antibody; POC3 centriolar protein homolog antibody; Prostate cancer antigen T21 antibody; rd16 antibody; SLSN6 1; 2; 5 antibody; SLSN6 antibody; Tumor antigen se2-2 antibody
Application:
ELISA, Western Blot
Buffer:
phosphate buffered saline (without mg2+ and ca2+)
Clonality:
Polyclonal
Extra Details:
Part of the tectonic-like complex which is required for tissue-specific ciliogenesis and may regulate ciliary membrane composition By similarity. Activates ATF4-mediated transcription. Required for the correct localization of ciliary and phototransduction proteins in retinal photoreceptor cells; may play a role in ciliary transport processes. ayer J.A., Nat. Genet. 38:674-681(2006). Nagase T., DNA Res. 4:141-150(1997). Scherer S.E., Nature 440:346-351(2006).
Host:
Rabbit
Immunogen:
Synthesized peptide derived from internal of Human CEP290.
Isotype:
IgG
Physical State:
Liquid
Purification:
Affinity Purified
Reactivities:
Human
Shipping Conditions:
Blue Ice
Storage Conditions:
-20[o]C/-70[o]C Avoid freeze/thaw cycles.
Supplier:
Cusabio
Type:
Antibody: Polyclonal Antibody