HMGCL Antibody
Product Sizes
50 ul
£186.00
CSB-PA576264-50UL
100 ul
£334.00
CSB-PA576264-100UL
About this Product
- SKU:
- CSB-PA576264
- Additional Names:
- 3 hydroxy 3 methylglutaryl CoA lyase antibody; 3 hydroxy 3 methylglutaryl Coenzyme A lyase antibody; 3 hydroxymethyl 3 methylglutaryl Coenzyme A lyase (hydroxymethylglutaricaciduria) antibody; 3 hydroxymethyl 3 methylglutaryl Coenzyme A lyase antibody; 3-hydroxy-3-methylglutarate-CoA lyase antibody; HL antibody; HMG CoA lyase antibody; HMG CoA Lyase Deficiency antibody; HMG-CoA lyase antibody; HMGCL antibody; HMGCL_HUMAN antibody; Hydroxymethylglutaricaciduria antibody; Hydroxymethylglutaryl CoA lyase antibody; Hydroxymethylglutaryl CoA lyase mitochondrial antibody; Hydroxymethylglutaryl-CoA lyase antibody; Mitochondrial 3 hydroxy 3 methylglutaryl CoA lyase antibody; mitochondrial antibody; MS725 antibody; OTTHUMP00000044830 antibody
- Application:
- ELISA, Immunohistochemistry, Western Blot
- Buffer:
- PBS
- Clonality:
- Polyclonal
- Extra Details:
- The protein encoded by this gene belongs to the HMG-CoA lyase family. It is a mitochondrial enzyme that catalyzes the final step of leucine degradation and plays a key role in ketone body formation. Mutations in this gene are associated with HMG-CoA lyase deficiency. Alternatively spliced transcript variants encoding different isoforms have been found for this gene.
- Host:
- Rabbit
- Immunogen:
- Fusion protein of Human HMGCL
- Isotype:
- IgG
- Physical State:
- Liquid
- Purification:
- Affinity Purified
- Reactivities:
- Human, Mouse, Rat
- Shipping Conditions:
- Blue Ice
- Storage Conditions:
- -20[o]C/-70[o]C Avoid freeze/thaw cycles.
- Supplier:
- Cusabio
- Type:
- Antibody: Polyclonal Antibody
- Manufacturer's Data Sheet:HMGCL-Antibody-11101518.html






