BEST1 Antibody
Product Sizes
50 ul
£186.00
CSB-PA269030-50UL
100 ul
£334.00
CSB-PA269030-100UL
About this Product
- SKU:
- CSB-PA269030
- Additional Names:
- ARB antibody; BEST 1 antibody; BEST antibody; Best disease antibody; Best macular dystrophy antibody; BEST1 antibody; BEST1_HUMAN antibody; Best1V1Delta2 antibody; Bestrophin 1 antibody; Bestrophin-1 antibody; Bestrophin1 antibody; BMD antibody; mBest1 antibody; RP50 antibody; TU15B antibody; Vitelliform macular dystrophy 2 antibody; Vitelliform macular dystrophy antibody; Vitelliform macular dystrophy protein 2 antibody; VMD 2 antibody; VMD2 antibody
- Application:
- ELISA, Immunohistochemistry, Western Blot
- Buffer:
- PBS
- Clonality:
- Polyclonal
- Extra Details:
- This gene encodes a member of the bestrophin gene family. This small gene family is characterized by proteins with a highly conserved N-terminus with four to six transmembrane domains. Bestrophins may form chloride ion channels or may regulate voltage-gated L-type calcium-ion channels. Bestrophins are generally believed to form calcium-activated chloride-ion channels in epithelial cells but they have also been shown to be highly permeable to bicarbonate ion transport in retinal tissue. Mutations in this gene are responsible for juvenile-onset vitelliform macular dystrophy (VMD2), also known as Best macular dystrophy, in addition to adult-onset vitelliform macular dystrophy (AVMD) and other retinopathies. Alternative splicing results in multiple variants encoding distinct isoforms.
- Host:
- Rabbit
- Immunogen:
- Synthetic peptide of Human BEST1
- Isotype:
- IgG
- Physical State:
- Liquid
- Purification:
- Affinity Purified
- Reactivities:
- Human, Mouse
- Shipping Conditions:
- Blue Ice
- Storage Conditions:
- -20[o]C/-70[o]C Avoid freeze/thaw cycles.
- Supplier:
- Cusabio
- Type:
- Antibody: Polyclonal Antibody
- Manufacturer's Data Sheet:BEST1-Antibody-11103273.html
