FBN1 Antibody

Product Sizes

50 ul

£186.00

CSB-PA107393-50UL

100 ul

£334.00

CSB-PA107393-100UL

About this Product

SKU:: CSB-PA107393
Additional Names:: 350 kDa glycoprotein component extracellular microfibril antibody; ACMICD antibody; FBN 1 antibody; FBN antibody; FBN1 antibody; FBN1_HUMAN antibody; Fibrillin 15 antibody; Fibrillin-1 antibody; Fibrillin1 antibody; Fibrillin15 antibody; GPHYSD2 antibody; Marfan syndrome antibody; MASS antibody; MFS 1 antibody; MFS1 antibody; OCTD antibody; SGS antibody; SSKS antibody; Weill Marchesani syndrome antibody; WMS antibody; WMS2 antibody
Application:: ELISA, Immunohistochemistry
Buffer:: PBS
Clonality:: Polyclonal
Extra Details:: This gene encodes a member of the fibrillin family. The encoded protein is a large, extracellular matrix glycoprotein that serve as a structural component of 10-12 nm calcium-binding microfibrils. These microfibrils provide force bearing structural support in elastic and nonelastic connective tissue throughout the body. Mutations in this gene are associated with Marfan syndrome, isolated ectopia lentis, autosomal dominant Weill-Marchesani syndrome, MASS syndrome, and Shprintzen-Goldberg craniosynostosis syndrome.
Host:: Rabbit
Immunogen:: Synthetic peptide of Human FBN1
Isotype:: IgG
Physical State:: Liquid
Purification:: Affinity Purified
Reactivities:: Human, Mouse
Shipping Conditions:: Blue Ice
Storage Conditions:: -20[o]C/-70[o]C Avoid freeze/thaw cycles.
Supplier:: Cusabio
Type:: Antibody: Polyclonal Antibody

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