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Antibodies

Anti-Frataxin (Mitochondrial Marker) Monoclonal Antibody(Clone: rFXN/2124)

Product Sizes
20 µg
£397.00
36-2332-20UG
100 µg
£716.00
36-2332-100UG
About this Product
SKU:
36-2332
Additional Names:
CyaY; d-FXN; FARR; Frataxin mature form; Frataxin (81-210); FRDA; Friedreich ataxia protein; Fxn; i-FXN; m56-FXN; m78-FXN; m81-FXN; X25
translate.label.attr.clone:
rFXN/2124
Clonality:
Monoclonal
Extra Details:
Frataxin is a nuclear-encoded mitochondrial protein implicated in Friedreich's ataxia (FRDA); a human autosomal recessive neurodegenerative disease. Lack of Frataxin causes iron to accumulate in the mitochondrial matrix sµggesting that Frataxin is involved in mitochondrial iron homeostasis and possibly in iron transport. Frataxin has an alpha-beta fold consisting of two helices flanking an antiparallel beta sheet.
Host:
Mouse
Immunogen:
Recombinant human Frataxin protein fragment (around aa 57-210) (exact sequence is proprietary)
Isotype:
Mouse IgG1; kappa
Reactivities:
Human
Shipping Conditions:
Blue Ice
Storage Conditions:
Antibody with azide - store at 2 to 8[o]C. Antibody without azide - store at -20 to -80[o]C. Antibody is stable for 24 months. Non-hazardous.
Supplier:
Abeomics
Type:
Antibodies:Monoclonal Antibody
  • Manufacturer's Data Sheet:1.jpg