Anti-Frataxin (Marker of Friedreich Ataxia) Monoclonal Antibody(Clone: FXN/2124)
Product Sizes
20 µg
£397.00
36-2331-20UG
100 µg
£716.00
36-2331-100UG
About this Product
- SKU:
- 36-2331
- Additional Names:
- CyaY; d-FXN; FARR; Frataxin mature form; Frataxin (81-210); FRDA; Friedreich ataxia protein; Fxn; i-FXN; m56-FXN; m78-FXN; m81-FXN; X25
- translate.label.attr.clone:
- FXN/2124
- Clonality:
- Monoclonal
- Extra Details:
- Frataxin is a nuclear-encoded mitochondrial protein implicated in Friedreich's ataxia (FRDA); a human autosomal recessive neurodegenerative disease. Lack of Frataxin causes iron to accumulate in the mitochondrial matrix sµggesting that Frataxin is involved in mitochondrial iron homeostasis and possibly in iron transport. Frataxin has an alpha-beta fold consisting of two helices flanking an antiparallel beta sheet.
- Host:
- Mouse
- Immunogen:
- Recombinant fragment of human Frataxin (FXN) protein (around aa 57-210) (exact sequence is proprietary)
- Isotype:
- Mouse IgG2b; kappa
- Reactivities:
- Human
- Shipping Conditions:
- Blue Ice
- Storage Conditions:
- Antibody with azide - store at 2 to 8[o]C. Antibody without azide - store at -20 to -80[o]C. Antibody is stable for 24 months. Non-hazardous.
- Supplier:
- Abeomics
- Type:
- Antibodies:Monoclonal Antibody
- Manufacturer's Data Sheet:1.jpg
