BCKDHA Recombinant Protein
Product Sizes
5 µg
£528.00
32-2179-5UG
About this Product
- SKU:
- 32-2179
- Additional Names:
- 2-oxoisovalerate dehydrogenase subunit alpha mitochondrial||Branched-chain alpha-keto acid dehydrogenase E1 component alpha chain||BCKDE1A||BCKDH E1-alpha||BCKDHA||MSU||MSUD1||OVD1A||FLJ45695.
- Extra Details:
- Source : Escherichia Coli. BCKDHA Human Recombinant fused with a 21 amino acid His tag at N-terminus produced in E.Coli is a single; non-glycosylated; polypeptide chain containing 421 amino acids (46-445 a.a.) and having a molecular mass of 47.8kDa. The BCKDHA is purified by proprietary chromatographic techniques. Branched-chain Alpha-keto acid dehydrogenase E1 component ? chain (BCKDHA) is a member of the BCKDHA family. The BCKD (branched-chain alpha-keto acid dehydrogenase) complex is an inner mitochondrial enzyme complex which catalyzes the second major step in the catabolism of the branched-chain amino acids leucine; isoleucine; and valine. This complex consists of 3 catalytic components: a heterotetrameric (alpha2-beta2) branched-chain alpha-keto acid decarboxylase (E1); a dihydrolipoyl transacylase (E2); and a dihydrolipoamide dehydrogenase (E3). Mutations in the BCKDHA gene result in maple syrup urine disease; type IA.
- Purification:
- Greater than 80.0% as determined by SDS-PAGE.
- Shipping Conditions:
- Blue Ice
- Storage Conditions:
- Store at 4[o]C if entire vial will be used within 2-4 weeks. Store; frozen at -20[o]C for longer periods of time. For long term storage it is recommended to add a carrier protein (0.1% HSA or BSA).Avoid multiple freeze-thaw cycles.
- Supplier:
- Abeomics
- Type:
- Proteins, Peptides, Small Molecules & Other Biomolecules
- Manufacturer's Data Sheet:1.jpg
