GTX88069
PEX26 antibody, Internal
Cannot supply to this region.
- SKU:
- GTX88069
- Additional Names:
- peroxisomal biogenesis factor 26 , PBD7A , PBD7B , PEX26M1T , Pex26pM1T
- Application:
- WB
- Concentration:
- 0.50 mg/ml
- Physical State:
- Liquid
- Species Reactivity:
- Human
- Purification:
- Ammonium Sulfate Precipitated; Affinity Purified
- Storage Conditions:
- -20[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., 2-8[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., -20[o]C/-70[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted.
- Supplier:
- Genetex
- Host:
- Goat
- Reactivities:
- Human
- Buffer:
- TBS, 0.5% BSA, 0.02% Sodium azide.
- Immunogen:
- Peptide with sequence C-QKPNLEGSVSHK, from the internal region of the protein sequence according to NP_060399.1.
- Uniprot:
- Q7Z412
- Synonyms:
- PBD7A;PBD7B;peroxin-26;peroxisome assembly protein 26;peroxisome biogenesis disorder, complementation group 8;peroxisome biogenesis disorder, complementation group A;peroxisome biogenesis factor 26;PEX26M1T;Pex26pM1T
- Extra Details:
- This gene belongs to the peroxin-26 gene family. It is probably required for protein import into peroxisomes. It anchors PEX1 and PEX6 to peroxisome membranes, possibly to form heteromeric AAA ATPase complexes required for the import of proteins into peroxisomes. Defects in this gene are the cause of peroxisome biogenesis disorder complementation group 8 (PBD-CG8). PBD refers to a group of peroxisomal disorders arising from a failure of protein import into the peroxisomal membrane or matrix. The PBD group is comprised of four disorders: Zellweger syndrome (ZWS), neonatal adrenoleukodystrophy (NALD), infantile Refsum disease (IRD), and classical rhizomelic chondrodysplasia punctata (RCDP). Alternatively spliced transcript variants have been identified for this gene. [provided by RefSeq, Dec 2010]
- Shipping Conditions:
- Blue Ice