IVD antibody [1B10]

Cannot supply to this region.

SKU:: GTX84285
Additional Names:: isovaleryl-CoA dehydrogenase , ACAD2
Application:: WB, IHC-P, IF, ICC
Concentration:: 1 mg/ml
Physical State:: Liquid
Species Reactivity:: Human
Purification:: Affinity Purified
Storage Conditions:: -20[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., 2-8[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., -20[o]C/-70[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted.
Supplier:: Genetex
Host:: Mouse
Reactivities:: Canine, Human, Rat
Buffer:: PBS, 1% BSA, 50% Glycerol, 0.02% Sodium azide.
Immunogen:: Full length human recombinant protein of human IVD (NP_002612) produced in HEK293T cell.
Clone:: 1B10
Uniprot:: P26440
Synonyms:: ACAD2;butyryl-CoA dehydrogenase;epididymis secretory sperm binding protein;isovaleryl Coenzyme A dehydrogenase;isovaleryl-CoA dehydrogenase, mitochondrial;IVDH
Extra Details:: Isovaleryl-CoA dehydrogenase (IVD) is a mitochondrial matrix enzyme that catalyzes the third step in leucine catabolism. The genetic deficiency of IVD results in an accumulation of isovaleric acid, which is toxic to the central nervous system and leads to isovaleric acidemia. Alternatively spliced transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq]