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  2. Polyclonal

GTX33205

FAH antibody

Cannot supply to this region.

SKU:
GTX33205
Additional Names:
fumarylacetoacetate hydrolase
Application:
WB, IF, ICC
Physical State:
Liquid
Species Reactivity:
Human
Purification:
Affinity Purified
Storage Conditions:
-20[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., 2-8[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., -20[o]C/-70[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted.
Supplier:
Genetex
Host:
Rabbit
Reactivities:
Human
Buffer:
PBS, 50% Glycerol, 0.02% Sodium azide.
Immunogen:
Recombinant fusion protein containing a sequence corresponding to amino acids 1-419 of human FAH (NP_000128.1).
Uniprot:
P16930
Synonyms:
beta-diketonase;epididymis secretory sperm binding protein;FAA;fumarylacetoacetase;Fumarylacetoacetate hydrolase;fumarylacetoacetate hydrolase (fumarylacetoacetase)
Extra Details:
This gene encodes the last enzyme in the tyrosine catabolism pathway. FAH deficiency is associated with Type 1 hereditary tyrosinemia (HT). [provided by RefSeq, Jul 2008]
Shipping Conditions:
Blue Ice