GTX134513
GLB1 antibody

Cannot supply to this region.
- SKU:
- GTX134513
- Additional Names:
- galactosidase, beta 1 , AW125515 , Bge , Bgl , Bgl-e , Bgl-s , Bgl-t , Bgs , Bgt , C130097A14Rik
- Application:
- WB
- Concentration:
- 0.87 mg/ml
- Physical State:
- Liquid
- Species Reactivity:
- Mouse
- Purification:
- Affinity Purified
- Storage Conditions:
- -20[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., 2-8[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., -20[o]C/-70[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted.
- Supplier:
- Genetex
- Host:
- Rabbit
- Reactivities:
- Mouse, Rat
- Buffer:
- PBS, 20% Glycerol, 0.025% ProClin 300.
- Immunogen:
- Carrier-protein conjugated synthetic peptide encompassing a sequence within the N-terminus region of mouse GLB1. The exact sequence is proprietary.
- Uniprot:
- P23780
- Synonyms:
- acid beta-galactosidase;AW125515;beta-galactosidase;Bg;Bge;Bgl;Bgl-;Bgl-e;Bgl-s;Bgl-t;Bgs;Bgt;C130097A14Rik;lactase
- Extra Details:
- This gene encodes a preproprotein that is proteolytically cleaved to yield a signal peptide and a proproptein that is subsequently processed to generate the active mature peptide. The encoded protein is a lysosomal enzyme that catalyzes the hydrolysis of terminal beta-D-galactose residues in various substrates like lactose, ganglioside GM1 and other glycoproteins. Mutations in the human gene are associated with GM1-gangliosidosis and Morquio B syndrome. Disruption of the mouse gene mirrors the symptoms of human gangliosidosis. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Dec 2013]
- Shipping Conditions:
- Blue Ice
