NAGLU antibody [N3C1], Internal

Cannot supply to this region.

SKU:: GTX114569
Additional Names:: N-acetyl-alpha-glucosaminidase , CMT2V , MPS-IIIB , MPS3B , NAG , UFHSD
Application:: WB, IHC-P, IF, ICC
Concentration:: 1 mg/ml
Physical State:: Liquid
Species Reactivity:: Human
Purification:: Affinity Purified
Storage Conditions:: -20[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., 2-8[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., -20[o]C/-70[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted.
Supplier:: Genetex
Host:: Rabbit
Reactivities:: Human, Mouse, Rat
Buffer:: 0.1M Tris, 0.1M Glycine, 20% Glycerol, 0.01% Thimerosal.
Immunogen:: Recombinant protein encompassing a sequence within the center region of human NAGLU. The exact sequence is proprietary.
Clone:: N3C1
Uniprot:: P54802
Synonyms:: alpha-N-acetylglucosaminidase;CMT2V;MPS-IIIB;MPS3B;N-acetyl-alpha-glucosaminidase;N-acetylglucosaminidase, alpha;NAG;testicular tissue protein Li 18;UFHSD
Extra Details:: This gene encodes an enzyme that degrades heparan sulfate by hydrolysis of terminal N-acetyl-D-glucosamine residues in N-acetyl-alpha-D-glucosaminides. Defects in this gene are the cause of mucopolysaccharidosis type IIIB (MPS-IIIB), also known as Sanfilippo syndrome B. This disease is characterized by the lysosomal accumulation and urinary excretion of heparan sulfate. [provided by RefSeq]