LMAN1 antibody [N1C1]

Cannot supply to this region.

SKU:: GTX114530
Additional Names:: lectin, mannose binding 1 , ERGIC-53 , ERGIC53 , F5F8D , FMFD1 , MCFD1 , MR60 , gp58
Application:: WB, IHC-P
Concentration:: 0.82 mg/ml
Physical State:: Liquid
Species Reactivity:: Human
Purification:: Affinity Purified
Storage Conditions:: -20[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., 2-8[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., -20[o]C/-70[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted.
Supplier:: Genetex
Host:: Rabbit
Reactivities:: Human
Buffer:: 0.1M Tris, 0.1M Glycine, 20% Glycerol, 0.01% Thimerosal.
Immunogen:: Recombinant protein encompassing a sequence within the center region of human LMAN1. The exact sequence is proprietary.
Clone:: N1C1
Uniprot:: P49257
Synonyms:: endoplasmic reticulum-golgi intermediate compartment protein 53;ER-Golgi intermediate compartment 53 kDa protein;ERGIC-53;ERGIC53;F5F8D;FMFD1;gp58;intracellular mannose-specific lectin MR60;Lectin mannose-binding 1;MCFD1;MR60;protein ERGIC-53
Extra Details:: The protein encoded by this gene is a type I integral membrane protein localized in the intermediate region between the endoplasmic reticulum and the Golgi, presumably recycling between the two compartments. The protein is a mannose-specific lectin and is a member of a novel family of plant lectin homologs in the secretory pathway of animal cells. Mutations in the gene are associated with a coagulation defect. Using positional cloning, the gene was identified as the disease gene leading to combined factor V-factor VIII deficiency, a rare, autosomal recessive disorder in which both coagulation factors V and VIII are diminished. [provided by RefSeq]

Shipping Conditions:: Blue Ice