![PPOX antibody [N3C3]](https://www.genetex.com/upload/website/prouct_img/normal/GTX106163/GTX106163_40562_WB_w_23060120_326.webp)
GTX106163
PPOX antibody [N3C3]
Cannot supply to this region.
- SKU:
- GTX106163
- Additional Names:
- protoporphyrinogen oxidase , PPO , V290M , VP
- Application:
- WB
- Concentration:
- 0.82 mg/ml
- Physical State:
- Liquid
- Species Reactivity:
- Human
- Purification:
- Affinity Purified
- Storage Conditions:
- -20[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., 2-8[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., -20[o]C/-70[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted.
- Supplier:
- Genetex
- Host:
- Rabbit
- Reactivities:
- Human
- Buffer:
- 0.1M Tris, 0.1M Glycine, 20% Glycerol, 0.01% Thimerosal.
- Immunogen:
- Recombinant protein encompassing a sequence within the center region of human PPOX. The exact sequence is proprietary.
- Clone:
- N3C3
- Uniprot:
- P50336
- Synonyms:
- PPO;protoporphyrinogen oxidase;V290M;VP
- Extra Details:
- This gene encodes the penultimate enzyme of heme biosynthesis, which catalyzes the 6-electron oxidation of protoporphyrinogen IX to form protoporphyrin IX. Mutations in this gene cause variegate porphyria, an autosomal dominant disorder of heme metabolism resulting from a deficiency in protoporphyrinogen oxidase, an enzyme located on the inner mitochondrial membrane. Alternatively spliced transcript variants encoding the same protein have been identified. [provided by RefSeq]
- Shipping Conditions:
- Blue Ice