UROS antibody [N1C3]

Cannot supply to this region.

SKU:: GTX105866
Additional Names:: uroporphyrinogen III synthase , UROIIIS
Application:: WB
Concentration:: 1 mg/ml
Physical State:: Liquid
Species Reactivity:: Human
Purification:: Affinity Purified
Storage Conditions:: -20[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., 2-8[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., -20[o]C/-70[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted.
Supplier:: Genetex
Host:: Rabbit
Reactivities:: Human
Buffer:: 0.1M Tris, 0.1M Glycine, 10% Glycerol, 0.01% Thimerosal.
Immunogen:: Recombinant protein encompassing a sequence within the center region of human UROS. The exact sequence is proprietary.
Clone:: N1C3
Uniprot:: P10746
Synonyms:: hydroxymethylbilane hydrolyase;Hydroxymethylbilane hydrolyase [cyclizing];UROIIIS;uroporphyrinogen-III cosynthase;uroporphyrinogen-III synthase
Extra Details:: The protein encoded by this gene catalyzes the fourth step of porphyrin biosynthesis in the heme biosynthetic pathway. Defects in this gene cause congenital erythropoietic porphyria (Gunther's disease). [provided by RefSeq]