PCCB antibody [N2C3]

Cannot supply to this region.

SKU:: GTX105204
Additional Names:: propionyl-CoA carboxylase subunit beta
Application:: WB, IHC-P, IF, ICC
Concentration:: 0.54 mg/ml
Physical State:: Liquid
Species Reactivity:: Human
Purification:: Affinity Purified
Storage Conditions:: -20[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., 2-8[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., -20[o]C/-70[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted.
Supplier:: Genetex
Host:: Rabbit
Reactivities:: Human, Mouse
Buffer:: 0.1M Tris, 0.1M Glycine, 10% Glycerol, 0.01% Thimerosal.
Immunogen:: Recombinant protein encompassing a sequence within the center region of human PCCB. The exact sequence is proprietary.
Clone:: N2C3
Uniprot:: P05166
Synonyms:: PCCase subunit beta;propanoyl-CoA:carbon dioxide ligase subunit beta;propionyl CoA carboxylase, beta polypeptide;propionyl Coenzyme A carboxylase, beta polypeptide;propionyl-CoA carboxylase beta chain, mitochondrial;propionyl-CoA carboxylase beta subunit
Extra Details:: The protein encoded by this gene is a subunit of the propionyl-CoA carboxylase (PCC) enzyme, which is involved in the catabolism of propionyl-CoA. PCC is a mitochondrial enzyme that probably acts as a dodecamer of six alpha subunits and six beta subunits. This gene encodes the beta subunit of PCC. Defects in this gene are a cause of propionic acidemia type II (PA-2). [provided by RefSeq]