![HADHB antibody [N1], N-term](https://www.genetex.com/upload/website/prouct_img/normal/GTX100302/GTX100302_39443_20220121_WB_w_23060100_143.webp)
GTX100302
HADHB antibody [N1], N-term
Cannot supply to this region.
- SKU:
- GTX100302
- Additional Names:
- hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit beta , ECHB , MSTP029 , MTPB , TP-BETA
- Application:
- WB
- Concentration:
- 1 mg/ml
- Physical State:
- Liquid
- Species Reactivity:
- Human
- Purification:
- Affinity Purified
- Storage Conditions:
- -20[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., 2-8[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., -20[o]C/-70[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted.
- Supplier:
- Genetex
- Host:
- Rabbit
- Reactivities:
- Human
- Buffer:
- PBS, 20% Glycerol, 0.01% Thimerosal.
- Immunogen:
- Carrier-protein conjugated synthetic peptide encompassing a sequence within the N-terminus region of human HADHB. The exact sequence is proprietary.
- Clone:
- N1
- Uniprot:
- P55084
- Synonyms:
- 2-enoyl-Coenzyme A (CoA) hydratase, beta subunit;3-ketoacyl-Coenzyme A (CoA) thiolase of mitochondrial trifunctional protein, beta subunit;acetyl-CoA acyltransferase;beta-ketothiolase;ECHB;hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), beta subunit;hydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), beta subunit;MSTP029;MTPB;TP-BETA;trifunctional enzyme subunit beta, mitochondrial
- Extra Details:
- This gene encodes the beta subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the beta subunit catalyzing the 3-ketoacyl-CoA thiolase activity. Mutations in this gene result in trifunctional protein deficiency. The encoded protein can also bind RNA and decreases the stability of some mRNAs. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation. Alternatively spliced transcript variants have been found; however, their full-length nature is not known. [provided by RefSeq]
- Shipping Conditions:
- Blue Ice