Human SOD1 protein (active)

Cannot supply to this region.

SKU:: GTX04316-PRO
Additional Names:: superoxide dismutase 1 , ALS , ALS1 , HEL-S-44 , IPOA , SOD , hSod1 , homodimer
Application:: FuncS
Physical State:: Lyophilized
Storage Conditions:: -20[o]C with carrier protein. Aliquot. Avoid freeze/thaw cycles., 2-8[o]C Aliquot. Avoid freeze/thaw cycles.
Supplier:: Genetex
Buffer:: Reconstitute with sterile H₂O but not less than 100 ug/ml. Lyophilized from 0.2um filtered concentrated solution in PBS pH 7.4, no preservatives.
Immunogen:: superoxide dismutase 1
Species:: Human
Uniprot:: P00441
Synonyms:: ALS;ALS1;Cu/Zn superoxide dismutase;epididymis secretory protein Li 44;HEL-S-44;homodimer;hSod1;indophenoloxidase A;IPOA;SOD;SOD, soluble;STAHP;superoxide dismutase [Cu-Zn];Superoxide dismutase 1;superoxide dismutase 1, soluble;superoxide dismutase, cystolic
Extra Details:: The protein encoded by this gene binds copper and zinc ions and is one of two isozymes responsible for destroying free superoxide radicals in the body. The encoded isozyme is a soluble cytoplasmic protein, acting as a homodimer to convert naturally-occuring but harmful superoxide radicals to molecular oxygen and hydrogen peroxide. The other isozyme is a mitochondrial protein. Mutations in this gene have been implicated as causes of familial amyotrophic lateral sclerosis. Rare transcript variants have been reported for this gene. [provided by RefSeq, Jul 2008]