alpha Sarcoglycan antibody [Ad1/20A6]

Cannot supply to this region.

SKU:: GTX01939
Additional Names:: sarcoglycan alpha , 50DAG , ADL , DAG2 , DMDA2 , LGMD2D , LGMDR3 , SCARMD1 , adhalin
Application:: IHC-Fr
Physical State:: Liquid
Species Reactivity:: Rabbit
Purification:: Unpurified
Storage Conditions:: 2-8[o]C Do not freeze.
Supplier:: Genetex
Host:: Mouse
Reactivities:: Hamster, Human, Mouse, Porcine, Rabbit, Rat
Buffer:: Tissue culture supernatant, 0.09% Sodium azide.
Immunogen:: Fusion protein containing amino acids 217 to 289 of the rabbit adhalin sequence (Roberds SL et al., 1993).
Clone:: Ad1/20A6
Uniprot:: Q16586
Synonyms:: 50 kDa dystrophin-associated glycoprotein;50DAG;50kD DAG;adhalin;ADL;alpha-sarcoglycan;alpha-SG;DAG2;DMDA2;dystroglycan-2;LGMD2D;LGMDR3;limb girdle muscular dystrophy 2D;sarcoglycan, alpha (50kDa dystrophin-associated glycoprotein);SCARMD1
Extra Details:: This gene encodes a component of the dystrophin-glycoprotein complex (DGC), which is critical to the stability of muscle fiber membranes and to the linking of the actin cytoskeleton to the extracellular matrix. Its expression is thought to be restricted to striated muscle. Mutations in this gene result in type 2D autosomal recessive limb-girdle muscular dystrophy. Multiple transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Oct 2008]