Skip to content
  1. Shop all

451084

Ganglioside GM2, Asialo

Size

POA

SKU:
451084
Molecular Weight:
1093.43
Purity:
≥95%
Storage Conditions:
-20°C
Supplier:
United States Biological
CAS Number:
35960-33-9
Format:
White to off-white powder
Extra Details:
Asialylated glycosphingolipid, which is also known as asialo-GM2 ganglioside. This compound accumulates in the cells of individuals with the Sandhoff disease, a lysosomal storage disorder, where β-hexosaminase is dysfunctional and unable to break down GA2 ganglioside to lactosylceramide (LacCer). Synonyms: CeCeramide trihexoside, Gangliotriosylceramide, Asialoganglioside-GM2; GgOse3Cer; b-GalNAc-(1→4)-b-Gal-(1→4)-b-Glc-(1→1')-Cer; 1-O-[O-2-(acetylamino)-2-deoxy-β-D-galactopyranosyl-(1→4)-O-β-D-galactopyranosyl-(1→4)-β-D-glucopyranosyl]-ceramide CAS No: 35960-33-9 Molecular Formula: C56H104N2O18 Molecular Weight: 1093.43 Appearance: White to off-white powder Purity: ≥95% Identity (1H NMR): Conforms to structure Solubility: Chloroform, Methanol Storage and Stability: Store at -20°C. For maximum recovery of product, centrifuge the original vial prior to removing the cap.
Shipping Conditions:
Ambient