376887
Glutaryl-L-Carnitine, Lithium Salt
Size
£347.00
- SKU:
- 376887
- Molecular Weight:
- 275.3
- Purity:
- ≥98% (TLC)
- Storage Conditions:
- 4°C
- Supplier:
- United States Biological
- CAS Number:
- 102636-82-8 (free acid)
- Format:
- Supplied as a white to off-white powder or crystals.
- Extra Details:
- A metabolite of L-Carnitine. Increased formation and excretion of glutarylcarnitin results from a glutaryl-CoA dehydrogenase deficiency, an inborn error of lysine and tryptophan metabolism. Secondary carnitine depletion due to increased formation and urinary excretion of glutarylcarnitine is suggested to play an important role in the neuropathogenesis of glutaryl-CoA dehydrogenase deficiency, inducing excitotoxic neuronal damage and mitochondrial dysfunction. Optical Activity: 20/D -20±2°, c = 1 in H2O Impurities: ≤10% water Storage and Stability: Store at 4°C. Stable for 6 months after receipt. For maximum recovery of product, centrifuge the original vial prior to removing the cap. Hygroscopic. Store under inert atmosphere.
- Shipping Conditions:
- Ambient