10-2413
Miglustat HCl
Size
£177.00
- SKU:
- 10-2413
- Additional Names:
- NB-DNJ
- Physical State:
- Solid
- Molecular Weight:
- 255.74
- Purity:
- 98%
- Storage Conditions:
- -20[o]C
- Supplier:
- Focus Biomolecules
- CAS Number:
- 210110-90-0
- Immunogen:
- Chaperone|Glycosylation
- Extra Details:
- Orally active ceramide-specific glycosyltransferase and A Alpha-glucosidase I and II inhibitor.1 Rescues trafficking-deficient F508del-CFTR in human airway epithelial cells via inhibition of ER A Alpha-glucosidases I and II.2 Pharmacological chaperone for glucocerebrosidase degradation.3 Clinically useful agent for Gaucher disease type 1.4 Stabilizes neurological disorders in Niemann-Pick disease type C.5
- Shipping Conditions:
- Ambient