E-AB-90948
PPT1 Polyclonal Antibody
Size
£195.30
Was £217.00
- SKU:
- E-AB-90948
- Additional Names:
- CLN1,INCL,PPT,PPT1
- Application:
- WB
- Concentration:
- 1 mg/ml
- Purification:
- Affinity Purified
- Storage Conditions:
- -20[o]C Avoid freeze/thaw cycles.
- Supplier:
- Elabscience
- Host:
- Rabbit
- Reactivities:
- Human, Mouse, Rat
- Buffer:
- Phosphate buffered solution, pH 7.4, containing 0.05% stabilizer and 50% glycerol.
- Immunogen:
- Recombinant fusion protein of human PPT1
- Uniprot:
- P50897
- Synonyms:
- ceroid-palmitoyl-palmitoyl-protein thioesterase 1;CLN1;INCL;palmitoyl-protein hydrolase 1;palmitoyl-protein thioesterase 1;PPT
- Extra Details:
- The protein encoded by this gene is a small glycoprotein involved in the catabolism of lipid-modified proteins during lysosomal degradation. The encoded enzyme removes thioester-linked fatty acyl groups such as palmitate from cysteine residues. Defects in this gene are a cause of infantile neuronal ceroid lipofuscinosis 1 (CLN1, or INCL) and neuronal ceroid lipofuscinosis 4 (CLN4). Two transcript variants encoding different isoforms have been found for this gene.
- Shipping Conditions:
- Blue Ice