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E-AB-66943

CASQ2 Polyclonal Antibody

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£195.30

Was £217.00

SKU:
E-AB-66943
Additional Names:
CASQ2,PDIB2
Application:
IHC
Concentration:
1 mg/ml
Purification:
Affinity Purified
Storage Conditions:
-20[o]C Avoid freeze/thaw cycles.
Supplier:
Elabscience
Host:
Rabbit
Reactivities:
Mouse, Rat
Buffer:
Phosphate buffered solution, pH 7.4, containing 0.05% stabilizer and 50% glycerol.
Immunogen:
Recombinant fusion protein of human CASQ2 (NP_001223.2).
Uniprot:
O14958
Synonyms:
calsequestrin 2 (cardiac muscle);calsequestrin 2, fast-twitch, cardiac muscle;calsequestrin-2;Calsequestrin, cardiac muscle isoform;PDIB2
Extra Details:
The protein encoded by this gene specifies the cardiac muscle family member of the calsequestrin family. Calsequestrin is localized to the sarcoplasmic reticulum in cardiac and slow skeletal muscle cells. The protein is a calcium binding protein that stores calcium for muscle function. Mutations in this gene cause stress-induced polymorphic ventricular tachycardia, also referred to as catecholaminergic polymorphic ventricular tachycardia 2 (CPVT2), a disease characterized by bidirectional ventricular tachycardia that may lead to cardiac arrest.
Shipping Conditions:
Blue Ice