E-AB-63961
PCCA Polyclonal Antibody
Size
£195.30
Was £217.00
- SKU:
- E-AB-63961
- Additional Names:
- PCCA
- Application:
- WB
- Concentration:
- 1 mg/ml
- Purification:
- Affinity Purified
- Storage Conditions:
- -20[o]C Avoid freeze/thaw cycles.
- Supplier:
- Elabscience
- Host:
- Rabbit
- Reactivities:
- Mouse, Rat
- Buffer:
- Phosphate buffered solution, pH 7.4, containing 0.05% stabilizer and 50% glycerol.
- Immunogen:
- Recombinant fusion protein of human PCCA (NP_000273.2).
- Uniprot:
- P05165
- Synonyms:
- pccA complementation group;PCCase alpha subunit;propanoyl-CoA:carbon dioxide ligase alpha subunit;Propanoyl-CoA:carbon dioxide ligase subunit alpha;propionyl CoA carboxylase, alpha polypeptide;propionyl Coenzyme A carboxylase, alpha polypeptide;propionyl-CoA carboxylase alpha chain, mitochondrial;propionyl-CoA carboxylase alpha subunit
- Extra Details:
- The protein encoded by this gene is the alpha subunit of the heterodimeric mitochondrial enzyme Propionyl-CoA carboxylase. PCCA encodes the biotin-binding region of this enzyme. Mutations in either PCCA or PCCB (encoding the beta subunit) lead to an enzyme deficiency resulting in propionic acidemia. Multiple transcript variants encoding different isoforms have been found for this gene.
- Shipping Conditions:
- Blue Ice