E-AB-63284
ETHE1 Polyclonal Antibody
Size
£195.30
Was £217.00
- SKU:
- E-AB-63284
- Additional Names:
- ETHE1,HSCO,YF13H12
- Application:
- IHC, WB, IF
- Concentration:
- 1 mg/ml
- Purification:
- Affinity Purified
- Storage Conditions:
- -20[o]C Avoid freeze/thaw cycles.
- Supplier:
- Elabscience
- Host:
- Rabbit
- Reactivities:
- Human, Mouse, Rat
- Buffer:
- Phosphate buffered solution, pH 7.4, containing 0.05% stabilizer and 50% glycerol.
- Immunogen:
- Recombinant fusion protein of human ETHE1 (NP_055112.2).
- Uniprot:
- O95571
- Synonyms:
- ethylmalonic encephalopathy 1;Ethylmalonic encephalopathy protein 1;hepatoma subtracted clone one protein;HSCO;persulfide dioxygenase ETHE1, mitochondrial;protein ETHE1, mitochondrial;sulfur dioxygenase ETHE1;YF13H12
- Extra Details:
- This gene encodes a member of the metallo beta-lactamase family of iron-containing proteins involved in the mitochondrial sulfide oxidation pathway. The encoded protein catalyzes the oxidation of a persulfide substrate to sulfite. Certain mutations in this gene cause ethylmalonic encephalopathy, an infantile metabolic disorder affecting the brain, gastrointestinal tract and peripheral vessels. Alternative splicing results in multiple transcript variants encoding different isoforms.
- Shipping Conditions:
- Blue Ice