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E-AB-53138

IDS Polyclonal Antibody

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£106.20

Was £118.00

SKU:
E-AB-53138
Additional Names:
AW214631,Alpha L iduronate sulfate sulfatase,Alpha-L-iduronate sulfate sulfatase,IDS,Ids,Iduronate 2 sulfatase,Iduronate 2 sulfatase 14 kDa chain,Iduronate 2 sulfatase 42 kDa chain,Iduronate 2-sulfatase 14 kDa chain,Iduronate sulfatase,Idursulfase,MPS2,RP
Application:
IHC
Concentration:
1.2 mg/ml
Purification:
Affinity Purified
Storage Conditions:
-20[o]C Avoid freeze/thaw cycles.
Supplier:
Elabscience
Host:
Rabbit
Reactivities:
Human, Mouse
Buffer:
Phosphate buffered solution, pH 7.4, containing 0.05% stabilizer and 50% glycerol.
Immunogen:
Fusion protein of human IDS
Uniprot:
P22304
Synonyms:
alpha-L-iduronate sulfate sulfatase;ID2S;iduronate 2-sulfatase;iduronate 2-sulfatase 14 kDa chain;iduronate 2-sulfatase 42 kDa chain;idursulfase;MPS2;SIDS
Extra Details:
Iduronate 2-sulfatase (IDS) is required for the lysosomal degradation of heparan sulfate and dermatan sulfate. Mutations causing IDS deficiency in humans result in the lysosomal storage of these glycosaminoglycans and Hunter syndrome,an X chromosome-linked disease. An internal proteolytic cleavage occurs to produce the mature IDS present in human liver shown to contain a 42 kDa polypeptide N-terminal to a 14 kDa polypeptide.
Shipping Conditions:
Blue Ice