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E-AB-14536

ALDH4A1 Polyclonal Antibody

Size

£106.20

Was £118.00

SKU:
E-AB-14536
Additional Names:
AL4A1,ALDH4,Aldehyde dehydrogenase,Aldehyde dehydrogenase family 4 member A1,Delta 1 pyrroline 5 carboxylate dehydrogenase,Delta-1-pyrro,aldehyde dehydrogenase 4,aldehyde dehydrogenase 4 family,aldh4a1,family 4,member 1,member A1,mitochondrial,subfamily A
Application:
IHC, WB
Concentration:
0.3 mg/ml
Purification:
Affinity Purified
Storage Conditions:
-20[o]C Avoid freeze/thaw cycles.
Supplier:
Elabscience
Host:
Rabbit
Reactivities:
Human, Mouse, Rat
Buffer:
Phosphate buffered solution, pH 7.4, containing 0.05% stabilizer and 50% glycerol.
Immunogen:
Recombinant protein of human ALDH4A1
Uniprot:
P30038
Synonyms:
aldehyde dehydrogenase family 4 member A1;ALDH4;delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial;epididymis secretory sperm binding protein;L-glutamate gamma-semialdehyde dehydrogenase;mitochondrial delta-1-pyrroline 5-carboxylate dehydrogenase;P5C dehydrogenase;P5CD;P5CDh
Extra Details:
This protein belongs to the aldehyde dehydrogenase family of proteins. This enzyme is a mitochondrial matrix NAD-dependent dehydrogenase which catalyzes the second step of the proline degradation pathway, converting pyrroline-5-carboxylate to glutamate. Deficiency of this enzyme is associated with type II hyperprolinemia, an autosomal recessive disorder characterized by accumulation of delta-1-pyrroline-5-carboxylate (P5C) and proline. Alternatively spliced transcript variants encoding different isoforms have been identified for this gene.
Shipping Conditions:
Blue Ice