E-AB-13533
PPOX Polyclonal Antibody
Size
£106.20
Was £118.00
- SKU:
- E-AB-13533
- Additional Names:
- MGC8485,PPO,PPOX,Protoporphyrinogen oxidase,V290M,VP,Variegate porphyria
- Application:
- IHC
- Concentration:
- 0.4 mg/ml
- Purification:
- Affinity Purified
- Storage Conditions:
- -20[o]C Avoid freeze/thaw cycles.
- Supplier:
- Elabscience
- Host:
- Rabbit
- Reactivities:
- Human, Mouse
- Buffer:
- Phosphate buffered solution, pH 7.4, containing 0.05% stabilizer and 50% glycerol.
- Immunogen:
- Synthetic peptide of human PPOX
- Uniprot:
- P50336
- Synonyms:
- PPO;protoporphyrinogen oxidase;V290M;VP
- Extra Details:
- This gene encodes the penultimate enzyme of heme biosynthesis, which catalyzes the 6-electron oxidation of protoporphyrinogen IX to form protoporphyrin IX.Mutations in this gene cause variegate porphyria, an autosomal dominant disorder of heme metabolism resulting from a deficiency in protoporphyrinogen oxidase, an enzyme located on the inner mitochondrial membrane.Alternatively spliced transcript variants encoding the same protein have been identified.
- Shipping Conditions:
- Blue Ice