Recombinant Collagen VI Monoclonal Antibody

Size

£221.40

Was £246.00

SKU:: AN301269L
Additional Names:: COL6A,BTHLM,UCHMD,COL6A1,BTHLM1,OPLL,UCHMD1,Collagen alpha-1(VI) chain,COL6A1
Application:: IHC
Concentration:: 0.2 mg/ml
Purification:: Protein A Purified
Storage Conditions:: -20[o]C Avoid freeze/thaw cycles.
Supplier:: Elabscience
Host:: Rabbit
Reactivities:: Human, Mouse, Rat
Buffer:: PBS, 50% glycerol, 0.05% Proclin 300, 0.05% protein protectant.
Immunogen:: Recombinant Human Collagen VI protein
Clone:: B1032
Uniprot:: P12109
Synonyms:: alpha 1 (VI) chain (61 AA);BTHLM1;collagen alpha-1(VI) chain;collagen VI, alpha-1 polypeptide;collagen, type VI, alpha 1;epididymis secretory sperm binding protein;OPLL;UCHMD1
Extra Details:: The collagens are a superfamily of proteins that play a role in maintaining the integrity of various tissues. Collagens are extracellular matrix proteins and have a triple-helical domain as their common structural element. Collagen VI is a major structural component of microfibrils. The basic structural unit of collagen VI is a heterotrimer of the alpha1(VI), alpha2(VI), and alpha3(VI) chains. The alpha2(VI) and alpha3(VI) chains are encoded by the COL6A2 and COL6A3 genes, respectively. The protein encoded by this gene is the alpha 1 subunit of type VI collagen (alpha1(VI) chain). Mutations in the genes that code for the collagen VI subunits result in the autosomal dominant disorder, Bethlem myopathy.