AN300786L
Recombinant SGSH Monoclonal Antibody
Size
£221.40
Was £246.00
- SKU:
- AN300786L
- Additional Names:
- SGSH,HSS,MPS3A,SFMD,N-Sulphoglucosamine Sulphohydrolase,Sulfoglucosamine Sulfamidase,Sulphamidase
- Application:
- WB
- Concentration:
- 0.2 mg/ml
- Purification:
- Protein A Purified
- Storage Conditions:
- -20[o]C Avoid freeze/thaw cycles.
- Supplier:
- Elabscience
- Host:
- Rabbit
- Reactivities:
- Human
- Buffer:
- PBS, 50% glycerol, 0.05% Proclin 300, 0.05% protein protectant.
- Immunogen:
- Recombinant Human SGSH protein
- Clone:
- B729
- Uniprot:
- P51688
- Synonyms:
- heparan sulfate sulfatase;HSS;MPS3A;mucopolysaccharidosis type IIIA;N-sulphoglucosamine sulphohydrolase;SFMD;sulfoglucosamine sulfamidase;sulphamidase
- Extra Details:
- This gene encodes the enzyme sulfamidase, one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with the lysosomal storage disease mucopolysaccaridosis IIIA, also known as Sanfilippo syndrome A, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined.
- Shipping Conditions:
- Blue Ice