AN300279P
Recombinant GCSH Monoclonal Antibody
Size
£361.80
Was £402.00
- SKU:
- AN300279P
- Additional Names:
- GCSH,GCE,NKH,Glycine cleavage system H protein,Glycine cleavage system H protein mitochondrial,Glycine cleavage system protein H,Glycine cleavage system protein H (aminomethyl carrier),Lipoic acid containing protein,mitochondrial,Mitochondrial glycine cleavage system H protein
- Application:
- IHC-P
- Concentration:
- 1 mg/ml
- Purification:
- Protein A Purified
- Storage Conditions:
- -20[o]C/-70[o]C Avoid freeze/thaw cycles., 2-8[o]C Avoid freeze/thaw cycles.
- Supplier:
- Elabscience
- Host:
- Rabbit
- Reactivities:
- Human
- Buffer:
- PBS
- Immunogen:
- Recombinant Human GCSH Protein
- Clone:
- B201
- Uniprot:
- P23434
- Synonyms:
- GCE;glycine cleavage system H protein, mitochondrial;glycine cleavage system protein H (aminomethyl carrier);lipoic acid-containing protein;mitochondrial glycine cleavage system H-protein;NKH
- Extra Details:
- Degradation of glycine is brought about by the glycine cleavage system, which is composed of four mitochondrial protein components: P protein (a pyridoxal phosphate-dependent glycine decarboxylase), H protein (a lipoic acid-containing protein), T protein (a tetrahydrofolate-requiring enzyme), and L protein (a lipoamide dehydrogenase). The protein encoded by this gene is the H protein, which transfers the methylamine group of glycine from the P protein to the T protein. Defects in this gene are a cause of nonketotic hyperglycinemia (NKH). Two transcript variants, one protein-coding and the other probably not protein-coding,have been found for this gene. Also, several transcribed and non-transcribed pseudogenes of this gene exist throughout the genome.
- Shipping Conditions:
- Blue Ice