AN200143P
Isovaleryl-CoA dehydrogenase/IVD Monoclonal Antibody

Size
£311.40
Was £346.00
- SKU:
- AN200143P
- Additional Names:
- ACAD,IVD,ACAD2,FLJ12715,FLJ34849,Isovaleryl CoA dehydrogenase,Isovaleryl Coenzyme A dehydrogenase,Isovaleryl-CoA dehydrogenase,mitochondrial
- Application:
- Flow Cytometry, WB, IF, ICC, IP
- Concentration:
- 1 mg/ml
- Purification:
- Protein A Purified
- Storage Conditions:
- -20[o]C/-70[o]C Avoid freeze/thaw cycles., 2-8[o]C Avoid freeze/thaw cycles.
- Supplier:
- Elabscience
- Host:
- Mouse
- Reactivities:
- Human
- Buffer:
- PBS
- Immunogen:
- Recombinant Human Isovaleryl-CoA dehydrogenase / IVD protein
- Clone:
- A991
- Uniprot:
- P26440
- Synonyms:
- ACAD2;butyryl-CoA dehydrogenase;epididymis secretory sperm binding protein;isovaleryl Coenzyme A dehydrogenase;isovaleryl-CoA dehydrogenase, mitochondrial;IVDH
- Extra Details:
- Isovaleryl-CoA dehydrogenase (IVD) is a mitochondrial matrix enzyme that catalyzes the third step in leucine catabolism. The genetic deficiency of IVD results in an accumulation of isovaleric acid, which is toxic to the central nervous system and leads to isovaleric acidemia. Alternatively spliced transcript variants encoding different isoforms have been found for this gene.
- Shipping Conditions:
- Blue Ice