A7647
BCS1L Rabbit polyclonal antibody
Size
£152.00
- SKU:
- A7647
- Additional Names:
- BCS|BCS1|BCS1L|BJS|FLNMS|GRACILE|h-BCS|h-BCS1|Hs.6719|MC3DN1|PTD
- Application:
- ELISA, WB, IHC-P, IF, ICC
- Molecular Weight:
- 48kDa
- Species Reactivity:
- Human
- Purification:
- Affinity Purified
- Storage Conditions:
- -20[o]C Avoid freeze/thaw cycles.
- Supplier:
- Abclonal
- Host:
- Rabbit
- Reactivities:
- Human, Mouse, Rat
- Immunogen:
- Recombinant protein (or fragment).This information is considered to be commercially sensitive.
- Formulation:
- Unmodified
- Sequence:
- RKGVQLGLVAFRRHYMITLEVPARDRSYAWLLSWLTRHSTRTQHLSVETSYLQHESGRISTKFEFVPSPGNHFIWYRGKWIRVERSREMQMIDLQTGTPWESVTFTALGTDRKVFFNILEEARELALQQEEGKTVMYTAVGSEWRPFGYPRRRRPLNSVVLQQGLADRIVRDVQEFIDNPKWYTDRGIPYRRGYLLYGPPGCGKSSFI
- Uniprot:
- Q9Y276
- Synonyms:
- BC1 (ubiquinol-cytochrome c reductase) synthesis-like;BCS;BCS1;BCS1-like protein;BJS;FLNMS;GRACILE;h-BCS;h-BCS1;Hs.6719;MC3DN1;mitochondrial chaperone BCS1;mitochondrial complex III assembly;PTD
- Extra Details:
- This gene encodes a homolog of the S. cerevisiae bcs1 protein which is involved in the assembly of complex III of the mitochondrial respiratory chain. The encoded protein does not contain a mitochondrial targeting sequence but experimental studies confirm that it is imported into mitochondria. Mutations in this gene are associated with mitochondrial complex III deficiency and the GRACILE syndrome. Several alternatively spliced transcripts encoding two different isoforms have been described.
- Shipping Conditions:
- Blue Ice