Skip to content

View Spec Sheet

open_in_new
  1. Shop all
  2. Monoclonal

A28496

OPA1 Rabbit monoclonal antibody

Size

POA

SKU:
A28496
Additional Names:
BERHS|largeG|MGM1|MTDPS14|NPG|NTG
Application:
ELISA, WB, IF, ICC, IP
Molecular Weight:
80-100 kDa
Species Reactivity:
Human
Purification:
Affinity Purified
Storage Conditions:
-20[o]C Avoid freeze/thaw cycles.
Supplier:
Abclonal
Host:
Rabbit
Reactivities:
Human, Mouse, Rat
Immunogen:
Recombinant protein (or fragment).This information is considered to be commercially sensitive.
Formulation:
Unmodified
Uniprot:
O60313
Synonyms:
BERHS;dynamin-like 120 kDa protein, mitochondrial;dynamin-like guanosine triphosphatase;largeG;MGM1;mitochondrial dynamin-like GTPase;MTDPS14;NPG;NTG;optic atrophy 1 (autosomal dominant);optic atrophy protein 1
Extra Details:
The protein encoded by this gene is a nuclear-encoded mitochondrial protein with similarity to dynamin-related GTPases. The encoded protein localizes to the inner mitochondrial membrane and helps regulate mitochondrial stability and energy output. This protein also sequesters cytochrome c. Mutations in this gene have been associated with optic atrophy type 1, which is a dominantly inherited optic neuropathy resulting in progressive loss of visual acuity, leading in many cases to legal blindness.
Shipping Conditions:
Blue Ice