A25015
OTC Rabbit monoclonal antibody

Size
POA
- SKU:
- A25015
- Additional Names:
- OCTD|OTC|OTC1|OTCase|OTCD
- Application:
- ELISA, WB, IF
- Molecular Weight:
- 36-40kDa
- Species Reactivity:
- Human
- Purification:
- Affinity Purified
- Storage Conditions:
- -20[o]C Avoid freeze/thaw cycles.
- Supplier:
- Abclonal
- Host:
- Rabbit
- Reactivities:
- Human, Mouse, Rat
- Immunogen:
- Recombinant protein (or fragment).This information is considered to be commercially sensitive.
- Formulation:
- Unmodified
- Sequence:
- LQAATPKGYEPDASVTKLAEQYAKENGTKLLLTNDPLEAAHGGNVLITDTWISMGQEEEKKKRLQAFQGYQVTMKTAKVAASDWTFLHCLPRKPEEVDDEVFYSPRSLVFPEAENRKWTIMAVMVSLLTDYSPQLQKPKF
- Uniprot:
- P00480
- Synonyms:
- OCTD;ornithine carbamoyltransferase, mitochondrial;Ornithine transcarbamylase;ornithine transcarbamylase, mitochondrial;OTCase;OTCD
- Extra Details:
- This nuclear gene encodes a mitochondrial matrix enzyme. The encoded protein is involved in the urea cycle which functions to detoxify ammonia into urea for excretion. Mutations in this enzyme lead to ornithine transcarbamylase deficiency, which causes hyperammonemia.
- Shipping Conditions:
- Blue Ice



