GTX81833
GNS antibody, Internal
Eine Lieferung in diese Region ist nicht möglich.
- SKU:
- GTX81833
- Zusätzliche Namen:
- glucosamine (N-acetyl)-6-sulfatase , G6S
- Anwendung:
- Flow Cytometry, WB, IHC-P
- Physischer Zustand:
- Liquid
- Spezies-Reaktivität:
- Human
- Aufreinigung:
- SAS Precipitated; Dialysis
- Lagerbedingungen:
- -20[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., 2-8[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., -20[o]C/-70[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted.
- Hersteller:
- Genetex
- Host:
- Rabbit
- Reaktivitäten:
- Human
- Buffer:
- PBS, 0.09% Sodium azide.
- Immunogen:
- KLH conjugated synthetic peptide between 283-313 amino acids from the Central region of human GNS.
- Uniprot:
- P15586
- Synonyme:
- G6S;glucosamine -6-sulfatase;Glucosamine-6-sulfatase;N-acetylglucosamine-6-sulfatase
- Weitere Details:
- The product of this gene is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome. [provided by RefSeq, Jul 2008]
- Versandbedingungen:
- Blue Ice