GTX64505
PCCA antibody
Eine Lieferung in diese Region ist nicht möglich.
- SKU:
- GTX64505
- Zusätzliche Namen:
- propionyl-CoA carboxylase subunit alpha
- Anwendung:
- WB
- Physischer Zustand:
- Liquid
- Spezies-Reaktivität:
- Human, Mouse
- Aufreinigung:
- Affinity Purified
- Lagerbedingungen:
- -20[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., 2-8[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., -20[o]C/-70[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted.
- Hersteller:
- Genetex
- Host:
- Rabbit
- Reaktivitäten:
- Mouse, Rat
- Buffer:
- PBS, 50% Glycerol, 0.02% Sodium azide.
- Immunogen:
- Recombinant fusion protein containing a sequence corresponding to amino acids 449-728 of human PCCA (NP_000273.2).
- Uniprot:
- P05165
- Synonyme:
- pccA complementation group;PCCase alpha subunit;propanoyl-CoA:carbon dioxide ligase alpha subunit;Propanoyl-CoA:carbon dioxide ligase subunit alpha;propionyl CoA carboxylase, alpha polypeptide;propionyl Coenzyme A carboxylase, alpha polypeptide;propionyl-CoA carboxylase alpha chain, mitochondrial;propionyl-CoA carboxylase alpha subunit
- Weitere Details:
- The protein encoded by this gene is the alpha subunit of the heterodimeric mitochondrial enzyme Propionyl-CoA carboxylase. PCCA encodes the biotin-binding region of this enzyme. Mutations in either PCCA or PCCB (encoding the beta subunit) lead to an enzyme deficiency resulting in propionic acidemia. Multiple transcript variants encoding different isoforms have been found for this gene.[provided by RefSeq, May 2010]
- Versandbedingungen:
- Blue Ice