SPG7 antibody [HL2236]

Eine Lieferung in diese Region ist nicht möglich.

SKU:: GTX638281
Zusätzliche Namen:: SPG7 matrix AAA peptidase subunit, paraplegin , CAR , CMAR , PGN , SPG5C
Anwendung:: WB, IHC-P, IF, ICC
Konzentration:: 1 mg/ml
Physischer Zustand:: Liquid
Spezies-Reaktivität:: Human
Aufreinigung:: Protein A Purified
Lagerbedingungen:: -20[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., 2-8[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., -20[o]C/-70[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted.
Hersteller:: Genetex
Host:: Rabbit
Reaktivitäten:: Human, Mouse, Rat
Buffer:: PBS, no preservatives.
Immunogen:: Recombinant fragmemt of human SPG7.
Klon:: HL2236
Uniprot:: Q9UQ90
Synonyme:: CAR;cell matrix adhesion regulator;CMAR;paraplegin;PGN;spastic paraplegia 7 (pure and complicated autosomal recessive);spastic paraplegia 7 protein;SPG5C;SPG7, paraplegin matrix AAA peptidase subunit
Weitere Details:: This gene encodes a mitochondrial metalloprotease protein that is a member of the AAA family. Members of this protein family share an ATPase domain and have roles in diverse cellular processes including membrane trafficking, intracellular motility, organelle biogenesis, protein folding, and proteolysis. Mutations in this gene cause autosomal recessive spastic paraplegia 7. Two transcript variants encoding distinct isoforms have been identified. [provided by RefSeq, Mar 2014]