GTX33308
MCCC2 antibody
Eine Lieferung in diese Region ist nicht möglich.
- SKU:
- GTX33308
- Zusätzliche Namen:
- methylcrotonoyl-CoA carboxylase 2 , MCCB
- Anwendung:
- WB, IHC-P
- Physischer Zustand:
- Liquid
- Spezies-Reaktivität:
- Human
- Aufreinigung:
- Affinity Purified
- Lagerbedingungen:
- -20[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., 2-8[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., -20[o]C/-70[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted.
- Hersteller:
- Genetex
- Host:
- Rabbit
- Reaktivitäten:
- Human, Mouse, Rat
- Buffer:
- PBS, 50% Glycerol, 0.02% Sodium azide.
- Immunogen:
- Recombinant fusion protein containing a sequence corresponding to amino acids 284-563 of human MCCC2 (NP_071415.1).
- Uniprot:
- Q9HCC0
- Synonyme:
- 3-methylcrotonyl-CoA carboxylase 2;3-methylcrotonyl-CoA carboxylase non-biotin-containing subunit;3-methylcrotonyl-CoA:carbon dioxide ligase subunit beta;biotin carboxylase;MCCase subunit beta;MCCB;MCCCbeta;methylcrotonoyl-CoA carboxylase 2 (beta);methylcrotonoyl-CoA carboxylase beta chain, mitochondrial;methylcrotonoyl-Coenzyme A carboxylase 2 (beta);non-biotin containing subunit of 3-methylcrotonyl-CoA carboxylase;testicular secretory protein Li 29
- Weitere Details:
- This gene encodes the small subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism. Alternative splicing results in multiple transcript variants encoding distinct isoforms. [provided by RefSeq, May 2018]
- Versandbedingungen:
- Blue Ice